Cardiovascular Research at Childrens Hospital Boston
The
focus of my research is the characterization of zebrafish mutations
that affect cardiac development. This work currently centers on the
study of three zebrafish mutants collectively referred to as the "big
hearts" (valentine, heart of glass,santa). The hearts are
huge, but thin-walled because the myocardium does not thicken as in the
normal heart. The number of cells is not altered, implicating a defect
in the concentric growth of the myocardium in these mutants. They have
endocardium, but do not develop endocardial cushions, which give rise to
valves.
The genes responsible for these mutations have been identified and we
are currently looking at the relationship between these newly defined
genes and the phenotype of the mutants. The similarity between the
phenotypes of the three big hearts suggests the intriguing possibility
of a common pathway. We can increase (by RNA injection) or decrease (by
antisense morpholino oligomer injection) expression of these genes in
the zebrafish, and together with biochemical approaches we hope to
define the interactions between them.
Two of these three genes have never been described previously, and none
of the three have been examined in the context of cardiac development.
In addition, the development of the zebrafish heart is very similar to
that of the early mammalian embryo so that any insights provided by this
work will be extendable to human studies with relevance for human
cardiac disease.